Generic Name
Alglucosidase Alpha EnzymePacks Price
- Inf 50 mg(088667): 1 Vial: 82963.67: 97604.32
Myozyme
Therapeutic Group
Other Alimentary Tract PrepsIndication Dosage
Alglucosidase alpha enzyme, also known as Alglucosidase alfa or enzyme replacement therapy (ERT), is a medication used to treat Pompe disease. Pompe disease is a rare genetic disorder that affects the muscles and can cause respiratory and cardiac failure. Alglucosidase alpha enzyme works by replacing the missing or deficient enzyme in patients with Pompe disease. The medication is administered intravenously, and the dosage and frequency of administration are determined by the patient's weight and the severity of the disease.
Long-term Enzyme Replacement Therapy (ert) In Pompe Disease (acid Alpha-glucosidase Deficiency):
By IV Infusion:
- Adult & Children: 20 Mg/kg Administered Once Every 2 Weeks, By Expert Physicians Only
Content
- Inf: Each Vial Contains 50mg Powder For Reconstitution For Infusion
Pregnancy
Risk Of Toxicity, But Treatment Should Not Be Withheld.
Stability
- Enzyme Produced By Recombinant Dna Technology
Contra Indications
- Life Threatening Hypersensitivity (anaphylactic Reaction) To The Substance
Precautions
- Life Threatening Hypersensitivity (anaphylactic Reaction) To The Substance
Lactation
- Avoid Breast Feeding During Treatment
Side Effects
- Arrhythmias
- Anxiety
- Dizziness
- Fatigue
- Chest Discomfort
- Chills
- Cough
- Cyanosis
- Diarrhoea
- Fever
- Hyperhidrosis
- Hypersensitivity
- Hypertension
- Irritability
- Oedema
- Pallor
- Paraesthesia
- Respiratory Disorders
- Skin Reactions
- Cough
- Tremor
- Nausea
- Vomiting
- Rare: Cardiac Arrest
- Angioedema
- Apnoea
- Arthralgia
- Dyspnoea
- Eye Inflammation
- Hypotension
- Nephrotic Syndrome
- Peripheral Coldness
- Proteinuria
- Vasoconstriction
Author
Shahid Arif